Mechanisms of Rare Unicuspid Aortic Valve With Predominant Aortic Regurgitation Uncovered by Multimodality Imaging

Unicuspid aortic valve (UAV) presented as predominant severe aortic regurgitation (AR) is rare (<1%) in pure AR cohort. We present a case with UAV that took more than 1 decade to achieve accurate diagnosis. Multimodality imaging showcased precise anatomy of UAV and mechanisms of AR, resembling exactly the surgical findings. (Level of Difficulty: Intermediate.).