Abstract
Primitive neuroectodermal tumours (PNETs) are a malignant group of neoplasms and are neuroectodermal in origin. In most large series published to date, peripheral primitive neuroectodermal tumours usually present in the second decade of life, with a slight male preponderance. Those which occurs peripherally resemble soft tissue sarcomas. Peripheral PNET is rare in presentation and of which only few cases involving the soft tissues of the abdominal wall have been reported. We present a case affecting a young female who presented to us with a progressively enlarging swelling involving the anterior abdominal wall. She underwent wide excision followed by adjuvant therapy based on final histopathology report.