Abstract
PURPOSE: To describe a patient of anterior clinoid mucocele presenting with orbital apex syndrome and to propose the reason for her unrecovered monocular vision loss after operation, we hope this case report can provide treatment experience for the similar rare disease. CONCLUSIONS AND IMPORTANCE: Mucocele of the anterior clinoid process remains a rare cause of optic neuropathy. They usually present with acute, rapidly progressive, painless monocular visual loss. Urgent surgical decompression play a vital role in the recovery of neurological function.