Abstract
Spinal arachnoid cyst (SAC) constitutes about less than 1% of all spinal tumors. It commonly occurs in third to fifth decades of life and mostly located in the thoracic region. Sacral extradural arachnoid cyst in the pediatric age group is an extremely rare location of occurrence. A such rare case of extradural arvwachnoid cyst of the sacral region, who presented with urinary incontinence is reported. The patient was managed surgically with laminectomy at S1-S3 vertebral level and complete excision of the extradural sacral arachnoid cyst with closure of transdural communication. The patient tolerated surgical procedure very well with regained bladder sphincter control at 6 months of follow-up. Early diagnosis and surgery are recommended for the treatment of symptomatic pediatric sacral arachnoid cysts.