Abstract
Guillain-Barré syndrome with ventricular septal defect is rare finding. Delayed diagnosis, often leading to increased complications. This report describes an Guillain-Barré syndrome case and the special approaches required during anaesthesia. 4 yrs old male pt with Guillain-Barré syndrome diagnosed at time of ward admission, submitted to video-assisted thoracic surgery under uneventful general anaesthesia with sevoflurane, without neuromuscular blockers. The case highlights the frequency with which this syndrome so important for anaesthetic practice is diagnosed, adverse events, the best choice for the anaesthetic team and complications of pediatric Guillain-Barré syndrome.