Abstract
A 9-month-old baby, born within the normal period of gestation and with normal psychomotor development, presented with a rapidly progressive small swelling persisting for several months and evolving towards an inflammatory status. CT scan of the orbit and brain after contrast injection showed right intraorbital tissue mass forcing the eyeball upwards and outwards. The patient underwent surgical biopsy of the lesion. The diagnosis was necrosed sarcomatous tumoral proliferation with undifferentiated cells of small size; immuno-histochemical examination revealed embryonic rhabdomyosarcome. The patient was lost to follow-up for 3 months, then re-consulted. MRI evaluation was requested. This showed a significant increase in tumor volume. Initial chemotherapy was recommended followed by locoregional radiotherapy. The baby died a few months later.