In silico prioritisation of EDN1 missense variants identifies mature endothelin-1 substitutions with predicted receptor-binding effects

通过计算机模拟对EDN1错义变异进行优先级排序,可以识别出具有预测受体结合效应的成熟内皮素-1替换。

阅读:3

Abstract

Endothelin-1 (ET-1) plays a major role in endothelial function and early vascular ageing (EVA). Although regulatory EDN1 variations have been investigated, it is unclear how missense mutations in the mature ET-1 peptide impact endothelin receptor binding. In this study, we aim to present a systematic in-silico prioritisation framework for EDN1 missense variants and generate structure-based hypotheses for substitutions in the mature ET-1 peptide that may disturb endothelin receptor binding. EDN1 nsSNPs from Ensembl/dbSNP were CADD/REVEL-filtered and assessed by standard pathogenicity, stability, and conservation/accessibility predictors using various tools, followed by short MD simulation. Out of 218 missense variants, integration of predictors identified 15 damaging nsSNPs, with 10 demonstrating consistent destabilisation. Four mutations correspond to the mature peptide: S4W, E10Q, C11R, and V12D. Compared to wild-type, all four showed reduced predicted ETBR binding, approximately 16–17% smaller interfaces, and a decrease in H-bonds. C11R exhibited the most significant disruption. S4W and E10Q resulted in intermediate effects, while V12D demonstrated the least disruption. STRING identified endothelin/renin–angiotensin and kinin-NO modules associated with vasoconstriction, blood pressure regulation, and ECM remodelling. Overall, these variants are computationally prioritised candidates for targeted functional validation. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1186/s12864-026-12687-x.

特别声明

1、本页面内容包含部分的内容是基于公开信息的合理引用;引用内容仅为补充信息,不代表本站立场。

2、若认为本页面引用内容涉及侵权,请及时与本站联系,我们将第一时间处理。

3、其他媒体/个人如需使用本页面原创内容,需注明“来源:[生知库]”并获得授权;使用引用内容的,需自行联系原作者获得许可。

4、投稿及合作请联系:info@biocloudy.com。