Abstract
A rare pediatric case report of middle ear neuroendocrine tumor and review of the pediatric cases reported in the literature. A 16-year-old female showed a lesion occupying the posterosuperior part of the medial third of the right external auditory canal confirmed by computed tomography scan, without clear evidence of bone erosion. The patient underwent canal wall tympanoplasty in 1 stage. No residual pathology was present after 1 month, 3-6 months, and after 1 year. There are few known pediatric cases of this disease, there is no statistically significant data for this population regarding the risk of recurrence or metastasis. Middle ear neuroendocrine tumors are rare above all in children. They are slow aggressive tumors but they can recur and rarely give local metástasis. Only 4 pediatric cases have been published. We have completely removed the tumor in our patient, using a conservative surgical treatment in a single stage.