Abstract
Type A aortic dissection is a life-threatening condition requiring urgent surgery. However, clinical experience with type A aortic dissection during twin pregnancy is extremely limited. We report a case of a 32-year-old woman with Marfan syndrome who was diagnosed with type A aortic dissection at 37 weeks of gestation with boy-girl twins. The patient successfully underwent caesarean delivery followed by aortic root replacement. Both the mother and twins were discharged without complications.