Abstract
Primary appendiceal neoplasms are uncommon, being found in approximately 0.5%-1.0% of appendectomy specimens at pathologic evaluation. Primary appendiceal Burkitt's lymphomas are rare occurring in 0.015% of all gastrointestinal lymphomas. Almost all reported cases of appendiceal lymphoma have proved to be non-Hodgkin lymphoma. The majority of appendiceal lymphomas are of B-cell. Patients were almost entirely males. Acute appendicitis is the most common clinical manifestation. This report describes a rare case of primary appendiceal lymphoma in a patient presented with hematuria and dull aching right lower abdominal and back pain.