Abstract
Cardiac rhabdomyoma is a rare benign tumor of the pediatric age group which usually regresses by the age of 2 years. Cardiac rhabdomyoma in adults is still a rarer disease. It is usually associated with tuberous sclerosis. Patients with cardiac rhabdomyoma will usually be asymptomatic and detected incidentally, or in suspicion to the signs and symptoms of tuberous sclerosis. Symptomatic patients present with palpitations or failure to thrive due to obstructive symptoms leading to cardiac failure. The authors present a rare case of right ventricular rhabdomyoma in an adult without tuberous sclerosis treated surgically.