Abstract
BACKGROUND: A vascular ring arises during the development of the fetal arches and is often associated with a double aortic arch or right-sided aorta, an aberrant left subclavian artery with a posterior esophageal component, and a left-sided ductus arteriosus. CASE SUMMARY: This is a rare vascular ring formed by a left aortic arch, aberrant right subclavian artery, and right ductus arteriosus that was diagnosed prenatally by fetal echocardiography. The 3-vessels and trachea (3VT) view with 2-dimensional and color Doppler sweeps were helpful in defining the vascular pathology. Tracheomalacia was also noted, and genetic tests confirmed the presence of 22q11.2 deletion. DISCUSSION: The distal portions of the right sixth and right eighth dorsal arches were persistent, whereas the right fourth and distal part of the left sixth arches disappeared in the process of fetal development. TAKE-HOME MESSAGE: Use of the 3VT echocardiography sweep facilitates prenatal diagnosis of rare vascular rings.