Abstract
Behçet's disease (BD) is a systemic vasculitis which manifests through diverse clinical manifestations, including oral and genital ulcers, and ocular lesions, and has potential for neurologic, gastrointestinal, and cardiovascular involvement. Coronary artery pseudoaneurysm is a very rare complication of BD. This paper presents the case of a giant coronary pseudoaneurysm presenting with acute coronary syndrome. Immunosuppressive therapy and coronary artery bypass grafting remain the most common treatment approach and are associated with excellent outcomes in surgically suitable candidates. This paper presents a case of a 27-year-old man with a history of BD presenting with acute coronary syndrome due to giant saccular coronary pseudoaneurysm.