Natural History of Double Inlet Left Ventricle and Pulmonary Hypertension in an Adult Patient

Almost 80% of univentricular cardiac malformations with left morphology consist of a double inlet left ventricle (DILV). We report on the natural history of a 28-year-old male patient with DILV and ventriculoarterial discordance, patent ductus arteriosus, pulmonary hypertension and juxtaductal aortic coarctation. (Level of Difficulty: Intermediate.).