Abstract
We describe a rare case of an optic pit located over the nasal portion of the disc that was independent of a coexisting optic nerve cyst. A healthy 35-year-old patient was referred to our clinic seeking alternative treatment options because his previous ophthalmologist had suggested evisceration and orbital surgery for a suspected orbital malignancy. Our examinations revealed a gray lesion located within the right disc cup that was associated with a round lesion at the retrobulbar optic nerve. Based on optical coherence tomography and magnetic resonance imaging findings, we believe that our patient exhibited an optic disc pit coexisting with a congenital optic nerve cyst. Because the patient had very good central vision and the lesions were benign, we recommended continued observation for this patient.