Abstract
Inflammatory myofibroblastic tumor is a rare occurring benign tumor composed of myofibroblastic spindle cells. Lung inflammatory myofibroblastic tumor is difficult to diagnose and may mimic lung cancer or infectious etiology. Surgical intervention with final histopathologic confirmation remains the mainstay of diagnosis. We report an incidental finding of a pediatric case of lung inflammatory myofibroblastic tumor with clinical presentation, management, and outcomes at more than 2 years of follow-up at a tertiary care hospital in Saudi Arabia.