Abstract
A 25-week preterm neonate was born with complete left-sided partial anomalous pulmonary venous drainage with a confluence draining into a vertical vein to the innominate vein. The ostium was stenotic, resulting in pulmonary hypertension requiring palliation by serial stent placement because of prematurity and comorbidities. The patient subsequently underwent successful surgical left anomalous pulmonary venous confluence reimplantation to the left atrium with vertical vein ligation at 12 months of age. This report highlights the unique multidisciplinary management strategy required for the rarely encountered obstructed complete left-sided anomalous pulmonary venous return in a preterm neonate.