Abstract
BACKGROUND: Lobar torsion is a rare and life-threatening condition where a lobe, segment, or the entire lung abnormally rotates. Therefore, timely diagnosis and appropriate management are crucial for favorable patient prognosis. CASE PRESENTATION: A 27-year-old female patient with a history of Marfan syndrome was under surveillance for a type B aortic dissection. She underwent open repair for a worsening aortic dissection. Her postoperative course was complicated by left upper lobe torsion, necessitating a subsequent left upper lobe lobectomy. CONCLUSIONS: In patients with risk factors for lung torsion identified during or after aortic dissection repair, prompt investigation and treatment of suspicious radiological findings are crucial for improving patient outcomes.