Abstract
BACKGROUND: Coarctation of the aorta (CoA) in adults is rare. usually combined with dilatation of the ascending aorta. Further disease progression complicated by hematoma or dissection of the ascending aorta is even more complicated and dangerous. CASE PRESENTATION: A 58-year-old male patient with CoA complicated by acute type A aortic intramural hematoma (IMH), who was treated with a two-stage hybrid approach involving an urgent Bentall repair procedure and subsequent endovascular stenting. A 4-year follow-up showed a good prognosis for the patient. CONCLUSION: For patients with aortic coarctation combined with ascending aortic dissection/IMH, life-threatening proximal aortic lesions may be treated first. Secondary stent implantation can then be performed after stabilization to treat the congenital aortic coarctation.