Abstract
Congenital anterior urethrocutanous fistula is a rare genitourinary malformation with unknown etiology and may present as an isolated form or in association with hypospadias or chordee. We describe a case of congenital anterior urethrocutanous fistula with chordee variants in a 5-year-old boy. The patient successfully underwent chordectomy and urethroplasty with no adverse outcomes. We report a review of the literature about the etiology and surgical intervention especially with chordee variants. The congenital anterior urethrocutanous fistula is a rare anomaly with unkown etiopathogenesis.