Abstract
INTRODUCTION AND IMPORTANCE: We present a case of Congenital fibular dimelia or fibula duplication with tibial hypoplasia, talar duplication and diplopodia with two complete pre-axial rays. This association has not been published in the literature to our knowledge. We discuss the unique features and surgical management of this rare condition. CASE PRESENTATION: The patient is a 3 year old child with congenital unilateral fibular dimelia, tibial hypoplasia, talar duplication and diplopodia who presented to us with leg length discrepancy and progressive equinovarus deformation of the right foot and ankle. She was surgically treated by excision of the medial two rays, cuneiforms, navicular, duplicate talus, os calcis and medial accessory fibula with reconstruction of the ankle joint capsule and foot reconstruction. DISCUSSION: Due to the rarity of the condition there is no described treatment protocol. It was decided to do resection taking in consideration of the disabling and unsightly progressive deformity. CONCLUSION: The case presented is a very rare of type of duplication deformity which we believe to be unique. The surgical treatment has been performed due to progressive deformity based on principles of management. Future follow up to observe growth and development of the lower limb joints, especially the ankle, as well as treatment for leg length equalization will be required.