Abstract
INTRODUCTION AND IMPORTANCE: Hirschprung's disease (HD) is a rare congenital colonic disorder that may develop in adult age, often determining a poor life quality with complications needing an emergency surgical setting. The disease rarely presents as an acute intestinal obstruction like SV, which represents an abdominal emergency issue. CASE PRESENTATION: A few days after discharge from gynecology unit because of her first childbirth, a young woman with HD developed colonic obstruction due to sigmoid volvulus, which was treated with Hartmann's procedure. CLINICAL DISCUSSION: Some months later, the patient underwent a two-stage Duhamel's procedure to restore the digestive tract's continuity. Both hospital periods were free of critical events. CONCLUSION: The woman regained a good quality of life: Duhamel's procedure revealed as a safe technique to use in HD adult.