Abstract
A 6-year-old child with Farber Lipogranulomatosis scheduled for dental procedures is a challenging case for safe, effective, and successful anaesthesia with well-communicated perioperative care. Farber disease presents unique challenges for anesthesiologists due to its multisystem involvement. The perioperative hazards of anesthesia were weighted higher than those of dental surgery due to multiple patient risk factors and conditions. Meticulous preoperative planning, careful airway management, and close postoperative monitoring ensured a successful outcome. Further research and case reports are needed to refine anesthetic strategies for this rare condition.