Abstract
Granulosa tumors are rare tumors arising from the cells of the sexual cord and stroma of the ovary. They account for 5% of ovarian cancers and 70% of stromal cancers of the sex cords. Retroperitoneal tumors (RPTs) are also rare and develop in the retroperitoneal and subperitoneal space. They are usually diagnosed late and are dominated by sarcomas and around 10% of teratomas. Based on principles derived from limb sarcoma surgery, compartmentectomy is currently the approach recommended by experts for the surgical removal of soft tissue sarcomas of the retroperitoneum. A primary retroperitoneal tumor composed of granulosa cells arising away from the ovaries, which is the usual location, is extremely rare. We describe a case of a left compartmental excision, removing the kidney and homolateral ureter, the left colon enlarged to the transverse with colorectal anastomosis for retroperitoneal granulosa tumor of the adult type in a 40-year-old woman.