Hypocretinergic dysfunction in neuromyelitis optica with coma-like episodes

视神经脊髓炎伴昏迷样发作中的下丘脑泌素能功能障碍

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Abstract

Devic's neuromyelitis optica (NMO) is a severe demyelinating disease of the central nervous system, often misdiagnosed as multiple sclerosis, and involving mainly optic nerves and the spinal cord. We report on a peculiar case of relapsing NMO with severe recurrent dysautonomia and hypersomnia, in which we had the opportunity to observe a dramatic decrease in hypocretin/orexin cerebrospinal fluid level.

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