Abstract
Neoplasms of testis are relatively rare with an incidence of approximately 1% of cancers in men diagnosed worldwide. Germ cell tumours form around more than 95% of testicular neoplasm. Primary synovial sarcoma of testis is exceedingly rare and soft tissue sarcoma forms around 1% of all adult malignancies. Among sarcomas, synovial sarcoma is about 5 to 10%. It is a mesenchymal tumour which affects children and young adults and mostly involves extremities. This is the second case being reported in the literature. We report the case of a 35-year-old man who presented with a left testicular mass and underwent radical high inguinal orchiectomy. Lost to follow-up, he returned with a recurrent mass in the left inguinoscrotal region. He underwent wide local excision with systemic chemotherapy (a combination of ifosfamide and doxorubicin)and radiotherapy postoperatively. He succumbed to the disease in a year. The prognosis is guarded as the optimal therapy is unknown.