Abstract
Ewing sarcoma is a malignant tumor that typically affects the appendicular skeleton; skull involvement is rare. Its clinical and radiological features are non-specific, making its diagnosis challenging. Confirmation is primarily achieved through immunohistochemistry. We report the case of a child who presented with facial swelling. MRI revealed an aggressive lesion involving the right sphenoid and temporal bones. Thoracic and abdominal CT scans showed no evidence of distant metastases. Biopsy of the lesion confirmed the diagnosis of Ewing sarcoma.