Abstract
Low-grade fibromyxoid sarcoma (LGFMS) is a soft tissue neoplasm that occurs preferentially in young, male adults as a slowly growing, asymptomatic mass. According to current literature, the most common anatomical sites where it occurs are the trunk and lower extremities, especially the thigh, perineum, and groin. The risk factors are still unknown. Surgical intervention (simple resection and wide excision) is nowadays considered the best treatment option; however, patients require a long follow-up due to the high recurrence and metastasis rates. We present a low-grade fibromyxoid sarcoma case located in the abdominal wall of a female Hispanic patient.