Abstract
Primary spindle cell sarcoma of the heart is a rare malignant tumor of the heart. A 65-year-old woman was admitted under our care with complaints of shortness of breath. Echocardiogram showed pedunculated mass in the left atrium. Cardiac magnetic resonance imaging done elsewhere had confirmed a left atrial tumor. No further investigations were considered with a diagnosis of left atrial myxoma. She underwent total excision of the tumor: mitral valve involvement necessitated a repair all of which was done under cardiopulmonary bypass. Histopathology showed a primary spindle cell sarcoma. In view of histology, chemotherapy was planned and initiated. A month after surgery, she presented again with a recurrence.