Abstract
Ewing sarcoma (ES) is a primitive neuroectodermal tumor usually located in the bones. The soft tissue as a primary localisation of ES is extremely rare. A few cases have been reported in the literature; the most affected areas are the head, trunk, neck, upper and lower limbs, or even multiple lesions. It is most often a painful and mobile subcutaneous swelling with a soft consistency; metastasis is very rare. Differential diagnosis is made with other small round cell neoplasms. Therapy for ES includes chemotherapy, radiation therapy, and surgery. In this paper, we discuss the findings of a soft tissue ewing sarcoma (STES) located in the right arm in a 14-year-old boy successfully treated in our department of pediatric surgery. The follow-up did not show any sign of recurrence after 24 months.