Abstract
Ewing's sarcoma itself is an uncommon disease. But its occurrence as a primary extraosseous cervical lesion is extremely rare. Considering the rarity of the manifestation of this disease in the form of a soft tissue mass in the neck, and the occurrence with nonspecific initial symptoms, this study introduces a patient whose only initial symptom was neck pain. The patient was a 23-year-old man who had been suffering from neck pain for ten days. Due to neck pain and 1 episode of urinary incontinence, the patient was hospitalized and examined. In the first 6 hours after admission, the patient experienced weakness of the upper limbs. A round lesion was seen in the alignment of the second vertebra with dimensions of 7 × 6 cm. Due to the progression of clinical symptoms, especially in the upper limbs, emergency surgery was planned for the patient. The diagnosis was Ewing's carcinoma. Tumoral cells were seen in diffuse form in small size with large nuclei, hyperchromatic and high N/C with large areas of necrosis. In conclusion, the urgency of surgical intervention in extraosseous Ewing sarcoma cannot be overstated, and it is essential for healthcare providers to remain vigilant in recognizing the signs of this aggressive disease to facilitate timely and effective treatment.