Abstract
RATIONALE: Low-grade malignant fibrous myxoid sarcoma (LGFMS) is a malignant tumor that originates from soft tissues and has specific clinical and histopathological characteristics. Paravertebral LGFMS is rarely reported. PATIENT CONCERNS: A 60-year-old woman had pain in the lower back and right anterior thigh for more than 3 years. DIAGNOSIS: Paravertebral LGFMS. INTERVENTIONS: Tumor resection, vertebral canal decompression and pedicle screw fixation. OUTCOMES: The tumor was excised, and the vertebral arch was fixed with pedicle screws at the root. Chemoradiotherapy was not performed. Her postoperative visual analogue scale (VAS) score decreased from 7 points at admission to 2 points at follow-up. The patient was discharged at postoperative day 13, and no recurrence was observed at the 6-month follow-up. LESSONS: Although LGFMS is rare, it should be considered in differential diagnosis of other soft tissue tumors to avoid misdiagnosis and inappropriate treatment.