Abstract
Cardiac rhabdomyomas are the most common primary cardiac tumors observed in neonates and children, which have been frequently associated with the tuberous sclerosis complex. These benign tumors usually have a natural history of regression but can sometimes cause significant clinical issues by obstructing blood flow and arrhythmias. We present an unusual case of a neonate who presented with a large cardiac rhabdomyoma with obstruction to the right ventricular inflow and outflow. The tumor necessitated an urgent surgery, which proved to be technically challenging.