Abstract
Primary renal teratomas are extremely rare germ cell tumors and can be difficult to distinguish from other fat-containing renal masses in infants using imaging alone. We report a case of a 3-month-old male with a right renal mass detected prenatally. Postnatal contrast-enhanced computed tomography revealed a well-circumscribed fat-containing lesion at the upper pole of the kidney. The patient underwent open nephron-sparing surgery with complete tumor enucleation. Histopathology confirmed a mature teratoma with negative margins. The postoperative course was uneventful, and at 1-year follow-up the child showed normal renal development with no evidence of recurrence.