Abstract
Neuroglial heterotopia (NH) is a rare entity which is composed of displaced masses of mature central neuroepithelial tissue manifesting in locations unconnected to the brain and spinal cord. NH is reported in the head and neck region, most commonly in the nose and nasopharynx, but some other rare sites, such as lung, extremities, and skin are also reported. NH presenting in the retroperitoneum and during infancy is extremely rare. We present a case of an infant who presented with lump abdomen and respiratory tract infection. Imaging revealed a large retroperitoneal tumour, which was safely excised. Histopathology revealed features of NH which was further confirmed by immunohistochemistry.