Fatal Sinus of Valsalva Aneurysm and Dissection into the Left Ventricle With Extension to the Interventricular Septum: A Challenging Diagnosis

• SVA is a rare condition caused by weakness of elastic lamina. • The right coronary sinus is involved in 67% to 85% of the reported cases. • Clinical features are varied and nonspecific, demanding a high index of suspicion. • Prompt diagnosis with echocardiography is recommended. • Emergent surgical repair should be offered to avoid clinical decompensation.