Abstract
Tolosa Hunt syndrome (THS) is characterized by painful ophthalmoplegia preceded by retro orbital headache. First described in year 1952, it is a diagnosis of exclusion and is extremely rare entity(.) Here we present a case report of syndrome in a female patient who presented with 03 weeks of progressive unilateral retro orbital headache followed by acute onset ptosis and complete ophthalmoplegia in right eye. On evaluation (brain imaging) and after ruling out all the other differentials, she was diagnosed as a case of THS. She was managed with parenteral corticosteroids followed by oral therapy. Patient showed remarkable response and complete recovery following 10 days of treatment. The follow-up brain imaging confirmed resolution of inflammation.