Abstract
Omphalocele is a congenital abdominal wall defect with herniation of abdominal viscera into a sac. Tc-99m DMSA renal cortical scan is a functional imaging technique used for detecting parenchymal defects, mostly in patients with recurrent urinary tract infection as well as congenital renal abnormalities. Renal anomalies are known to accompany omphalocele. In this retrospective study, we present a case of cephalad renal ectopia as observed on Tc-99m DMSA scintigraphy in a patient with omphalocele due to a large hernia sac containing most of the liver; and we review the renal abnormalities associated with omphalocele in the literature.