Abstract
Aphallia or penile agenesis is a rare case of the genitourinary system which has an association with upper urinary tract disorder. Failure of fetal genital tubercle formation in the embryonic period is the cause of this disorder. The incidence of aphallia according to previous studies is about 1 in 10-30 million births. We report a case of a child with the absence of the penis with associated kidney hypoplasia and vesicorectal fistula.