Abstract
Arteriovenous malformations in the mediastinum are rare and extremely unusual in middle mediastinum. The present report describes a 26-year male with spontaneous massive hemoptysis due to arteriovenous malformation in middle mediastinum and successful management by endovascular embolization. Spontaneous massive hemoptysis can be a presenting feature of arteriovenous malformation in middle mediastinum and endovascular embolization can be curative.