Abstract
Fibromuscular dysplasia is a rare, non-atherosclerotic non-inflammatory vascular disease that most commonly involves the renal arteries and carotid arteries, but has been described in nearly every vascular bed in the body. Complications of fibromuscular dysplasia include aneurysms and vascular dissection. We present a rare case of fibromuscular dysplasia involving the aorta, complicated by type A aortic dissection.