Abstract
Hughes-Stovin syndrome represents an exceptionally rare vasculitis disorder, with significant clinical convergence with Behçet's disease. The syndrome is defined by the coexistence of venous thromboembolism and pulmonary artery anevrysms. Intracardiac thrombi although rare, predominates within the right sided cardiac chambers. We report the case of a 30-year-old male patient with a prior diagnosis of Behçet's disease, presenting to emergency department with acute respiratory distress and echocardiographic signs of acute pulmonary heart and 2 large thrombi in the right ventricle, chest scan revealed bilateral pulmonary artery anevrysms along with alveolar hemorrhagic foci and recurrent pulmonary embolism. Through this case, we explore whether Hughes-Stovin syndrome represents a distinct clinical entity or a cardiovascular complication of Behçet's disease, and examine the therapeutic approaches associated with this emerging pattern.