Abstract
PURPOSE: To describe the formation of posterior staphyloma in a retinitis pigmentosa (RP) patient. OBSERVATIONS: A 5-year-old girl with RP and high myopia developed posterior staphyloma after 2 years. In the 2 years following this, the edges of the staphyloma deepened, and the staphyloma extended toward the posterior pole. The posterior staphyloma presented as a narrow macular type. During follow-up, staphyloma deepening was accompanied by axial elongation and increased myopic refractive error. CONCLUSIONS AND IMPORTANCE: This case highlights the onset and progression of posterior staphyloma in patients with RP, demonstrating that staphyloma related to RP occurs even in childhood.