Abstract
PURPOSE: To report a case of bilateral idiopathic chorioretinal folds that seemed to be related to an atypical staphyloma. OBSERVATIONS: A 49-year old man without medical history consulted for slight vision loss and metamorphopsia in the left eye. The ophthalmologic examination revealed moderate myopia and bilateral chorioretinal folds in the posterior pole, confirmed by multimodal imaging. Orbital and systemic examinations ruled out all the known etiologies of chorioretinal folds. 3-D optical coherence tomography and B-scan suggested that the folds were related to an atypical staphyloma that developed in the temporal part of the fundus, while sparing the peripapillary area. The peripapillary area, spared by the staphyloma process, appeared as a "dome-shaped disc" compared to the staphylomatous area. CONCLUSION AND IMPORTANCE: This case suggests that myopic patients with unusual staphyloma located outside the peripapillary area could develop chorioretinal folds.