Abstract
INTRODUCTION AND IMPORTANCE: Chordoid glioma is an extremely rare, slow-growing brain tumor. This report discusses the clinical presentation, imaging characteristics, surgical approach, histopathology, and prognosis. The review of literature provides an overview focusing on diagnostic challenges and treatment strategies. CASE PRESENTATION: A 21-year-old male presented with progressive blurring of vision, headache and intermittent convulsive seizures over a period of 2 months. Computerized tomography and magnetic resonance imaging revealed a mass in the right lateral ventricle, possibilities of central neurocytoma or ganglioglioma. Surgical resection was performed, and histopathological examination confirmed the diagnosis of chordoid glioma through a combination of histological and immunohistochemical analyses. CLINICAL DISCUSSION: Chordoid glioma is a distinct clinicopathologic entity, recognized for its unique histological and immunohistochemical features. It is crucial to differentiate chordoid gliomas from other neoplasms due to differences in treatment approaches and prognosis. CONCLUSION: Chordoid glioma, although rare, should be considered in the differential diagnosis of lateral ventricular tumors, especially in young adults presenting with visual and neurological symptoms. Early diagnosis and surgical intervention are crucial for improving outcomes.