Large sized bilateral adrenal myelolipoma with spontaneous retroperitoneal hemorrhage: a case series

双侧肾上腺髓脂肪瘤伴自发性腹膜后出血:病例系列

阅读:1

Abstract

INTRODUCTION: Adrenal myelolipomas are rare, benign adrenal tumors typically discovered incidentally. Histologically, it comprises mature adipose tissue and normal hematopoietic elements (erythroid, myeloid, and megakaryocytic precursors). Although often asymptomatic, larger tumors may present with mass effect, retroperitoneal hemorrhage, or spontaneous rupture requiring surgical intervention. CASE PRESENTATION: Both patients, a 51-year-old male and a 57-year-old female, presented with left-sided flank pain and imaging findings of large left adrenal masses (>10 cm) with retroperitoneal hemorrhage. Hormonal assays were negative, ruling out functional adrenal tumors. In both cases, laparoscopic adrenalectomy was attempted but converted to open surgery due to tumor size, friability, and intraoperative challenges. Bilateral adrenal myelolipoma and dense adhesion with the tail of the pancreas and splenic hilum was present in the first case. DISCUSSION: Spontaneous rupture of large-sized adrenal myelolipoma occurs, primarily in tumors >10 cm, leading to hemorrhagic events. Imaging, particularly CT and MRI, aids diagnosis, revealing characteristic fat-rich lesions. Management depends on size, symptoms, and imaging findings. Tumors <10 cm are typically treated laparoscopically, while larger or invasive ones require open surgery. The prognosis is excellent, with minimal follow-up needed for most cases. For large tumors, periodic ultrasounds and clinical reviews are advised post-surgery. CONCLUSION: Most cases of adrenal myelolipomas are small, unilateral, and non-adherent to adjacent structures, but some may be bilateral, large, or adherent to nearby organs, leading to symptoms and intraoperative challenges. This case series emphasizes the complications associated with large adrenal myelolipomas and underscores the importance of careful evaluation, planning, and surgical approach.

特别声明

1、本页面内容包含部分的内容是基于公开信息的合理引用;引用内容仅为补充信息,不代表本站立场。

2、若认为本页面引用内容涉及侵权,请及时与本站联系,我们将第一时间处理。

3、其他媒体/个人如需使用本页面原创内容,需注明“来源:[生知库]”并获得授权;使用引用内容的,需自行联系原作者获得许可。

4、投稿及合作请联系:info@biocloudy.com。