Abstract
BACKGROUND: Hydatid cyst is a common zoonotic condition in endemic areas. Intraventricular hydatid cyst is a rare entity with less than 50 cases published in literature. Floating water lily sign (also called Camalote sign) is very rare in intracranial hydatid cysts. Only a single case report of this sign exists in literature in intraventricular hydatidosis suggesting rupture of hydatid cyst leading to CSF dissemination and frequent poor outcome. CASE DESCRIPTION: This case report describes the successful management of a 5-year-old child who presented with signs and symptoms of raised intracranial pressure due to large intraventricular hydatid cyst in the right frontal horn, and magnetic resonanace imaging of the brain showed hydatid cyst with typical camalote sign. CONCLUSION: Although very rare, the presence of camalote sign in intraventricular cysts is very categorical in establishing preoperative diagnosis of hydatid cyst, especially in endemic areas.