Abstract
We present the case of a newborn male with congenital amniotic band syndrome and a constriction band involving the right inguinal crease, scrotum and perineum. He was diagnosed prenatally and referred to our institution after developing a right femoral nerve palsy. Surgical management included excision of the constriction band and Z-plasty closure. We discuss the considerations for safe and cosmetic surgical outcomes in this rare presentation of amniotic band syndrome. A multidisciplinary approach to management is essential during workup and surgical intervention.