Abstract
Zinner syndrome is a congenital anomaly characterized by seminal vesicle cysts, ipsilateral renal agenesis, and ejaculatory duct obstruction possibly associated with infertility. Only 200 cases of Zinner syndrome have been reported since its discovery in 1914. We present the case of a 63-year-old man seeking treatment for a ureteropelvic junction stone causing severe hydronephrosis. After the patient's history and the computed tomography findings were reviewed, the diagnosis of Zinner syndrome was confirmed. The patient has been nearly asymptomatic and has had three children during his lifetime. Our case could serve as a reference for future diagnoses of this rare anomaly.