Abstract
Hydatid disease (HD) is a parasitic endemic zoononis in Tunisia, caused by the larval stage of Echinococcus Granulosus (EG). Adrenal glands are an uncommon and rare location for hydatid cysts, even in endemic areas, and primary adrenal cysts are exceptional. Herein, we report a rare case of 46-year-old man with primary giant adrenal hydatid cyst complicated by inferior vena cava thrombosis. The patient was successfully treated with an open adrenalectomy, with prophylactic albendazole therapy pre and postoperatively.